IgG4-related Disease Manifesting as Autoimmune Pancreatitis, Sialadenitis, and Cholangitis: Case Report
Case studies
Augustina Tumelytė
Lithuanian University of Health Sciences image/svg+xml
Vytautas Rimkus
Lithuanian University of Health Sciences image/svg+xml
https://orcid.org/0009-0006-5481-0721
Paulina Tekoriutė
Lithuanian University of Health Sciences image/svg+xml
Limas Kupčinskas
Lithuanian University of Health Sciences image/svg+xml
https://orcid.org/0000-0002-8689-9023
Published 2025-08-25
https://doi.org/10.15388/Amed.2025.32.2.11
PDF
HTML

Keywords

IgG4-related disease
autoimmune pancreatitis
sialadenitis
cholangitis

How to Cite

1.
Tumelytė A, Rimkus V, Tekoriutė P, Kupčinskas L. IgG4-related Disease Manifesting as Autoimmune Pancreatitis, Sialadenitis, and Cholangitis: Case Report. AML. 2025;32(2):11. doi:10.15388/Amed.2025.32.2.11

Abstract

IgG4-related disease (IgG4-RD) is a rare autoimmune disease which can affect almost any organ. We present a case of IgG4-RD, which manifested as chronic autoimmune pancreatitis with pancreatic insufficiency, severe malnutrition, autoimmune sialadenitis, and cholangitis. After the administration of prednisolone and mycophenolate mofetil, the patient’s condition improved significantly.

PDF
HTML
Creative Commons License

This work is licensed under a Creative Commons Attribution 4.0 International License.

Downloads

Download data is not yet available.