Low-grade Appendiceal Mucinous Neoplasm (Appendiceal Villous Adenoma) with Cystic Fibrosis: A Case Report
Klinikinė praktika
Emrah Doğan
Muğla Sıtkı Koçman University, Turkey
Hakan Hakan Avcı
Ayvalik State Hospital, Turkey
Muge Kuzu Avcı
Ayvalik State Hospital, Turkey
Korkut Bozkurt
Muğla Milas State Hospital, Turkey
Ozge Oral Tapan
Muğla Sıtkı Koçman University, Turkey
Utku Tapan
Muğla Sıtkı Koçman University, Turkey
Publikuota 2021-04-16
https://doi.org/10.15388/LietChirur.2021.20.38
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Kaip cituoti

1.
Doğan E, Hakan Avcı H, Avcı MK, Bozkurt K, Tapan OO, Tapan U. Low-grade Appendiceal Mucinous Neoplasm (Appendiceal Villous Adenoma) with Cystic Fibrosis: A Case Report. LS [Internet]. 2021 Apr. 16 [cited 2024 Mar. 29];20(1):27-31. Available from: https://www.zurnalai.vu.lt/lietuvos-chirurgija/article/view/23884

Santrauka

Cystic fibrosis (CF) is an autosomal dominant disease characterized by the dysfunction of exocrine secretory glands resulting from a mutation in the transmembrane regulator protein (CFTR) gene. As life expectancy increases in patients with cystic fibrosis secondary to advances in treatment, advanced age malignancies secondary to cystic fibrosis emerge. Especially, the frequency of gastrointestinal system malignancies and colon cancers increases with aging. Appendiceal tumors are a rare entity and constitute less than 1% of gastrointestinal tumors. We presented a villous adenoma encountered in an 18-year-old male patient with CF accompanied by clinical and radiological findings. Our case is the first reported appendiceal tumor that emerged in patients with cystic fibrosis.

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